Malignant peripheral nerve sheath tumor
Human disease
A malignant peripheral nerve sheath tumor (MPNST) is a form of cancer of the connective tissue surrounding peripheral nerves. It is classified as a sarcoma. About half the cases are diagnosed in people with neurofibromatosis.[1] MPNST with rhabdomyoblastomatous component are called malignant triton tumors.
References
change- ↑ Evans DG, Baser ME, McGaughran J, Sharif S, Howard E, Moran A (May 2002). "Malignant peripheral nerve sheath tumours in neurofibromatosis 1". Journal of Medical Genetics. 39 (5): 311–314. doi:10.1136/jmg.39.5.311. PMC 1735122. PMID 12011145.
